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Acute interstitial pneumonia

MedGen UID:
224822
•Concept ID:
C1279945
•
Disease or Syndrome
Synonyms: Acute interstitial pneumonitis; Hamman-Rich syndrome
SNOMED CT: Acute interstitial pneumonia (236302005); Acute interstitial pneumonitis (35037009)
Modes of inheritance:
Unknown inheritance
MedGen UID:
989040
•Concept ID:
CN307042
•
Finding
Source: Orphanet
Hereditary clinical entity whose mode of inheritance is unknown.
See: This record
Unknown inheritance (Orphanet)
 
Monarch Initiative: MONDO:0019203
Orphanet: ORPHA79126

Definition

A rare rapidly progressive and histologically distinct form of idiopathic interstitial pneumonia. [from ORDO]

Professional guidelines

PubMed

Trastuzumab Deruxtecan‒Related Interstitial Lung Disease/Pneumonitis: Computed Tomography Imaging Patterns to Guide Diagnosis and Management.
Nishino M, Kusumoto M, Bankier AA, Kurihara Y, Zhang L, Rasheed Z, Meinhardt G, Arunachalam M, Taitt C, Wang Q, Powell CA
JCO Precis Oncol 2023 Sep;7:e2300391. doi: 10.1200/PO.23.00391. PMID: 38061008
Immune Checkpoint Inhibitor Therapy-related Pneumonitis: Patterns and Management.
Kalisz KR, Ramaiya NH, Laukamp KR, Gupta A
Radiographics 2019 Nov-Dec;39(7):1923-1937. Epub 2019 Oct 4 doi: 10.1148/rg.2019190036. PMID: 31584861
Advances in the treatment of rheumatic interstitial lung disease.
Vassallo R, Thomas CF
Curr Opin Rheumatol 2004 May;16(3):186-91. doi: 10.1097/00002281-200405000-00004. PMID: 15103243

Recent clinical studies

Etiology

Imaging Features of Idiopathic Interstitial Lung Diseases.
Batra K, Adams TN
J Thorac Imaging 2023 Nov 1;38(Suppl 1):S19-S29. Epub 2023 Jul 12 doi: 10.1097/RTI.0000000000000728. PMID: 37505195
SUCCESSFULLY TREATED ACUTE INTERSTITIAL PNEUMONIA.
Gomerčić Palčić M, Turalija I, Vrbanić L, Folnožić I, Basioli Kasap E, Ulamec M
Acta Clin Croat 2022 Dec;61(4):722-726. doi: 10.20471/acc.2022.61.04.21. PMID: 37868166Free PMC Article
Acute Interstitial Pneumonia (Hamman-Rich Syndrome) in Lung Transplantation: A Case Series.
Shepherd HM, Terada Y, Takahashi T, Pasque MK, Kulkarni HS, Guillamet RV, Witt CA, Nava RG, Puri V, Kreisel D, Patterson GA, Hachem RR
Transplant Proc 2022 Oct;54(8):2313-2316. Epub 2022 Sep 6 doi: 10.1016/j.transproceed.2022.07.010. PMID: 36075742
Fibrotic Idiopathic Interstitial Lung Disease: The Molecular and Cellular Key Players.
Samarelli AV, Tonelli R, Marchioni A, Bruzzi G, Gozzi F, Andrisani D, Castaniere I, Manicardi L, Moretti A, Tabbì L, Cerri S, Beghè B, Dominici M, Clini E
Int J Mol Sci 2021 Aug 19;22(16) doi: 10.3390/ijms22168952. PMID: 34445658Free PMC Article
Idiopathic interstitial pneumonias.
Silva CI, Müller NL
J Thorac Imaging 2009 Nov;24(4):260-73. doi: 10.1097/RTI.0b013e3181c1a9eb. PMID: 19935223

Diagnosis

Fibrotic Idiopathic Interstitial Lung Disease: The Molecular and Cellular Key Players.
Samarelli AV, Tonelli R, Marchioni A, Bruzzi G, Gozzi F, Andrisani D, Castaniere I, Manicardi L, Moretti A, Tabbì L, Cerri S, Beghè B, Dominici M, Clini E
Int J Mol Sci 2021 Aug 19;22(16) doi: 10.3390/ijms22168952. PMID: 34445658Free PMC Article
Immune Checkpoint Inhibitor Therapy-related Pneumonitis: Patterns and Management.
Kalisz KR, Ramaiya NH, Laukamp KR, Gupta A
Radiographics 2019 Nov-Dec;39(7):1923-1937. Epub 2019 Oct 4 doi: 10.1148/rg.2019190036. PMID: 31584861
What every radiologist should know about idiopathic interstitial pneumonias.
Mueller-Mang C, Grosse C, Schmid K, Stiebellehner L, Bankier AA
Radiographics 2007 May-Jun;27(3):595-615. doi: 10.1148/rg.273065130. PMID: 17495281
Acute interstitial pneumonia.
Vourlekis JS
Clin Chest Med 2004 Dec;25(4):739-47, vii. doi: 10.1016/j.ccm.2004.07.001. PMID: 15564019
Acute interstitial pneumonia.
Bouros D, Nicholson AC, Polychronopoulos V, du Bois RM
Eur Respir J 2000 Feb;15(2):412-8. doi: 10.1034/j.1399-3003.2000.15b31.x. PMID: 10706513

Therapy

SUCCESSFULLY TREATED ACUTE INTERSTITIAL PNEUMONIA.
Gomerčić Palčić M, Turalija I, Vrbanić L, Folnožić I, Basioli Kasap E, Ulamec M
Acta Clin Croat 2022 Dec;61(4):722-726. doi: 10.20471/acc.2022.61.04.21. PMID: 37868166Free PMC Article
Acute Interstitial Pneumonia (Hamman-Rich Syndrome) in Lung Transplantation: A Case Series.
Shepherd HM, Terada Y, Takahashi T, Pasque MK, Kulkarni HS, Guillamet RV, Witt CA, Nava RG, Puri V, Kreisel D, Patterson GA, Hachem RR
Transplant Proc 2022 Oct;54(8):2313-2316. Epub 2022 Sep 6 doi: 10.1016/j.transproceed.2022.07.010. PMID: 36075742
Immune Checkpoint Inhibitor Therapy-related Pneumonitis: Patterns and Management.
Kalisz KR, Ramaiya NH, Laukamp KR, Gupta A
Radiographics 2019 Nov-Dec;39(7):1923-1937. Epub 2019 Oct 4 doi: 10.1148/rg.2019190036. PMID: 31584861
Acute and subacute idiopathic interstitial pneumonias.
Taniguchi H, Kondoh Y
Respirology 2016 Jul;21(5):810-20. Epub 2016 Apr 28 doi: 10.1111/resp.12786. PMID: 27123874
Acute interstitial pneumonia.
Vourlekis JS
Clin Chest Med 2004 Dec;25(4):739-47, vii. doi: 10.1016/j.ccm.2004.07.001. PMID: 15564019

Prognosis

Immune Checkpoint Inhibitor Therapy-related Pneumonitis: Patterns and Management.
Kalisz KR, Ramaiya NH, Laukamp KR, Gupta A
Radiographics 2019 Nov-Dec;39(7):1923-1937. Epub 2019 Oct 4 doi: 10.1148/rg.2019190036. PMID: 31584861
Idiopathic interstitial pneumonias.
Silva CI, Müller NL
J Thorac Imaging 2009 Nov;24(4):260-73. doi: 10.1097/RTI.0b013e3181c1a9eb. PMID: 19935223
Acute interstitial pneumonia and acute exacerbations of idiopathic pulmonary fibrosis.
Swigris JJ, Brown KK
Semin Respir Crit Care Med 2006 Dec;27(6):659-67. doi: 10.1055/s-2006-957337. PMID: 17195142
Acute interstitial pneumonia.
Vourlekis JS
Clin Chest Med 2004 Dec;25(4):739-47, vii. doi: 10.1016/j.ccm.2004.07.001. PMID: 15564019
Acute interstitial pneumonia.
Bouros D, Nicholson AC, Polychronopoulos V, du Bois RM
Eur Respir J 2000 Feb;15(2):412-8. doi: 10.1034/j.1399-3003.2000.15b31.x. PMID: 10706513

Clinical prediction guides

Trastuzumab Deruxtecan‒Related Interstitial Lung Disease/Pneumonitis: Computed Tomography Imaging Patterns to Guide Diagnosis and Management.
Nishino M, Kusumoto M, Bankier AA, Kurihara Y, Zhang L, Rasheed Z, Meinhardt G, Arunachalam M, Taitt C, Wang Q, Powell CA
JCO Precis Oncol 2023 Sep;7:e2300391. doi: 10.1200/PO.23.00391. PMID: 38061008
Acute Interstitial Pneumonia (Hamman-Rich Syndrome) in Lung Transplantation: A Case Series.
Shepherd HM, Terada Y, Takahashi T, Pasque MK, Kulkarni HS, Guillamet RV, Witt CA, Nava RG, Puri V, Kreisel D, Patterson GA, Hachem RR
Transplant Proc 2022 Oct;54(8):2313-2316. Epub 2022 Sep 6 doi: 10.1016/j.transproceed.2022.07.010. PMID: 36075742
Expression of airway smooth muscle contractile proteins in children with acute interstitial pneumonia.
Cheng F, Lu T, Wang Y, Yuan D, Wei Z, Li Y, Li J, Tang R
Int J Exp Pathol 2022 Oct;103(5):190-197. Epub 2022 May 8 doi: 10.1111/iep.12443. PMID: 35527237Free PMC Article
Immune Checkpoint Inhibitor Therapy-related Pneumonitis: Patterns and Management.
Kalisz KR, Ramaiya NH, Laukamp KR, Gupta A
Radiographics 2019 Nov-Dec;39(7):1923-1937. Epub 2019 Oct 4 doi: 10.1148/rg.2019190036. PMID: 31584861
Reconsideration of discrepancies between clinical and histopathological features in acute eosinophilic pneumonia.
Mochimaru H, Fukuda Y, Azuma A, Osanai K, Saito Y, Mochimaru T, Gemma A
Sarcoidosis Vasc Diffuse Lung Dis 2015 Jan 5;31(4):325-35. PMID: 25591144

Recent systematic reviews

Acute exacerbation of idiopathic pulmonary fibrosis: a systematic review.
Agarwal R, Jindal SK
Eur J Intern Med 2008 Jun;19(4):227-35. Epub 2008 Jan 16 doi: 10.1016/j.ejim.2007.04.024. PMID: 18471669

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